This article summarized the nursing intervention measures for a patient with Fabry disease mainly manifested as proteinuria,including the implementation of enzyme replacement therapy nursing,multi-system function monitoring and nursing,dietary and lifestyle guidance,and psychological nursing.At the same time,multiple system assessments were conducted on the kidney,nervous system,cardiovascular system,etc.,and a multi system disease management system covering multidisciplinary collaboration,graded follow-up,self-management guidance,and health record management was established.After targeted nursing interventions and multi-system evaluations,the patient's condition was effectively controlled and no serious complications occurred.

Fabry disease  /  proteinuria  /  enzyme replacement therapy  /  multi-system evaluation  /  nursing